Volume 8, Issue 1, March 2020, Page: 16-19
A Rare Cause of Hemoptysis in Patients with Behcet's Disease: Hughes-stovin Syndrome: About One Case
Amine El Masloumi, Radiology Department, Arrazy Hospital, Mohammed VIth Teaching Center, Cadi Ayad University, Marrakesh, Morocco
Jean Frederic Adjimabou, Radiology Department, Arrazy Hospital, Mohammed VIth Teaching Center, Cadi Ayad University, Marrakesh, Morocco
Anass Chehboun, Radiology Department, Arrazy Hospital, Mohammed VIth Teaching Center, Cadi Ayad University, Marrakesh, Morocco
Badr Boutakioute, Radiology Department, Arrazy Hospital, Mohammed VIth Teaching Center, Cadi Ayad University, Marrakesh, Morocco
Meriem Ouali Idrissi, Radiology Department, Arrazy Hospital, Mohammed VIth Teaching Center, Cadi Ayad University, Marrakesh, Morocco
Najat Cherif Idrissi El Ganouni, Radiology Department, Arrazy Hospital, Mohammed VIth Teaching Center, Cadi Ayad University, Marrakesh, Morocco
Received: Feb. 18, 2020;       Accepted: Feb. 28, 2020;       Published: Mar. 17, 2020
DOI: 10.11648/j.ijmi.20200801.13      View  132      Downloads  35
Abstract
Hughes-Stovin Syndrome (HSS) is a very rare condition characterized by pulmonary aneurysms and peripheral thrombophlebitis of lower limbs. The pathogenesis of Hughes Stovin Syndrome is unknown. It’s considered as a clinical variant of Behçet’s disease. The main clinical manifestation is haemoptysis and dyspnea. The management of HSS can either be medical or surgical. We report the case of a young patient of 25 years old followed for Bechet's disease, who presents for a medium abundance hemoptysis with a swelling of the lower limbs evolving for 20 days, the radiological investigations made it possible to pose the diagnosis of the Syndrome of Huges-Stovin showing thrombosed aneurysms of the pulmonary arteries with thrombophlebitis of the lower limbs, the patient benefited from an immunosuppressive treatment, the evolution was marked by a good clinical evolution.
Keywords
Behcet, Pulmonary Aneurysms, Thrombophlebitis, Hugues-stovin
To cite this article
Amine El Masloumi, Jean Frederic Adjimabou, Anass Chehboun, Badr Boutakioute, Meriem Ouali Idrissi, Najat Cherif Idrissi El Ganouni, A Rare Cause of Hemoptysis in Patients with Behcet's Disease: Hughes-stovin Syndrome: About One Case, International Journal of Medical Imaging. Vol. 8, No. 1, 2020, pp. 16-19. doi: 10.11648/j.ijmi.20200801.13
Copyright
Copyright © 2020 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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